購物車
幫助
021-54845833/15800441009
中文名稱 : 兔抗PEX7多克隆抗體
英文名稱 : Anti-PEX7 rabbit polyclonal antibody
別 名 : RD; PBD9B; PTS2R; RCDP1
儲 存 : 冷凍（-20℃） 避光
抗 原 : PEX7
宿 主 : Rabbit
反應種屬 : Human Mouse
相關類別 : 一抗
標 記 物 : Unconjugate
克隆類型 : rabbit polyclonal
技術規(guī)格
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Background: |
This gene encodes the cytosolic receptor for the set of peroxisomal matrix enzymes targeted to the organelle by the peroxisome targeting signal 2 (PTS2). Defects in this gene cause peroxisome biogenesis disorders (PBDs), which are characterized by multiple defects in peroxisome function. There are at least 14 complementation groups for PBDs, with more than one phenotype being observed in cases falling into particular complementation groups. Although the clinical features of PBD patients vary, cells from all PBD patients exhibit a defect in the import of one or more classes of peroxisomal matrix proteins into the organelle. Defects in this gene have been associated with PBD complementation group 11 (PBD-CG11) disorders, rhizomelic chondrodysplasia punctata type 1 (RCDP1), and Refsum disease (RD). |
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Applications: |
WB, IHC |
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Name of antibody: |
PEX7 |
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Immunogen: |
Synthesized peptide derived from internal of human PEX7. |
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Full name: |
peroxisomal biogenesis factor 7 |
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Synonyms： |
RD; PBD9B; PTS2R; RCDP1 |
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SwissProt: |
O00628 |
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IHC positive control: |
Human breast carcinoma tissue |
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IHC Recommend dilution: |
50-100 |
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WB Predicted band size: |
36 kDa |
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WB Positive control: |
NIH/3T3 cells lysate |
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WB Recommended dilution: |
500-3000 |
